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020 _a9783030190552
024 7 _a10.1007/978-3-030-19055-2
_2doi
040 _aES-MaUEC
_bspa
_cES-MaUEC
_dES-MaUEC
050 4 _aRB129
_b.P475 2020 EB
245 0 0 _aPeriodic and Non-Periodic Fevers
_cedited by Rolando Cimaz
250 _aFirst edition
264 1 _aCham
_bSpringer International Publishing :
_bImprint: Springer
_c2020.
300 _a1 recurso en línea (X, 283 páginas)
_b38 ilustraciones, 32 ilustraciones a color
336 _2rdacontent
_aTexto
_btxt
337 _2rdamedia
_aelectrónico
_bc
338 _2rdacarrier
_arecurso electrónico
_bcr
347 _atext file
_bPDF
490 0 _aRare Diseases of the Immune System
_x2282-6505
490 0 _aMedicine (Springer-11650)
505 0 _aPreface -- I From Pathogenesis to Classification -- 1 Historical notes on Autoinflammatory disorders -- 2 Pathogenesis:Genetic basis, Innate Immunity, Inflammosomes, Cytokines -- 3 Classification and nomenclature of Periodic and Non Periodic fevers -- II Specific diseases -- 4 Mevalonate Kinase Deficiency (MKD) -- 5 Tumor necrosis factor receptors associated syndrome (TRAPS) -- 6 Cryopyrin-Associated Periodic Syndromes (CAPS) -- 7 Pyogenic Arthritis, Pyoderma gangrenosum and Acne Syndrome (PAPA) -- 8 Adenosine deaminase syndrome 2 (ADA2) -- 9 Interferonopathies -- 10 Inflammatory bone disease -- 11 Amyloidosis -- 12 Dermatologic autoinflammatory diseases -- 13 Autoinflammatory diseases with immunodeficiency -- 14 Periodic Fever, Aphthous Stomatitis, Pharyngitis, Adenitis Syndrome (PFAPA) -- 15 Proteasome. related disorders -- 16 Chronic Non-bacterial osteomyelitis -- 17 Systemic JIA and adult onset Still disease -- 18 Behcet disease -- 19 Recurrent idiopathic pericarditis -- 20 Schnitzler syndrome -- Subject Index.
520 3 _aThis book, written by very well-known opinion leaders in the field, covers all aspects of periodic and non -periodic fevers, and related disorders. The expression refers to several different auto-inflammatory diseases, showing similar symptoms-the primary symptom being a recurrent fever for an infectious cause cannot be found. The opening chapters give some historical hints, explain the genetic basis of the disease and provide insights into the pathogenesis derived from recent experimental studies and guides the reader through classification and nomenclature. A large part of the book is then devoted to a detailed description of the specific related diseases and their clinical presentations, the disease course, and potential complications in both pediatric and adult patients. The advice regarding treatment is based on the best currently available evidence in this constantly evolving area. The book is part of Springer's series Rare Diseases of the Immune System, which presents recently acquired knowledge on pathogenesis, diagnosis, and therapy with the aim of promoting a more holistic approach to these conditions. Autoinflammatory diseases are hereditary disorders that are caused by single-gene defects in innate immune regulatory pathways and are characterized by a clinical and biological inflammatory syndrome in which there is limited, if any, evidence of autoimmunity. Periodic and Non-Periodic Fevers will be an invaluable source of up-to-date information for all practitioners involved in the care of patients with these disease.
650 7 _2embne
_9672626
_aFiebre
700 1 _aCimaz, Rolando.
_eeditor
_4edt
_4http://id.loc.gov/vocabulary/relators/edt
_995211
710 2 _aSpringerLink (Online service)
_9106937
776 0 8 _iPrinted edition:
_z9783030190545
776 0 8 _iPrinted edition:
_z9783030190569
776 0 8 _iPrinted edition:
_z9783030190576
856 4 0 _uhttps://go.openathens.net/redirector/universidadeuropea.es?url=https://doi.org/10.1007/978-3-030-19055-2
_zAcceso a este recurso digital (usuarios Universidad Europea de Valencia)
942 _2lcc
_cLE
_n0
998 _db
_zSI